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KMID : 0358920110380010068
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Journal of the Korean Academy of Pedodontics
2011 Volume.38 No. 1 p.68 ~ p.74
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RETT SYNDROME : CASE REPORT
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Kong Eun-kyung
Hong So-Yi
Mah Yon-Joo
Ahn Byung-Duk
Jung Young-Jung
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Abstract
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Rett syndrome is a X-linked genetic neurological disorder characterized by developmental regression, particularly in relation to expressive language and use of the hands, together with profound mental retardation, that almost exclusively affects females. Oral manifestations of the disease are commonly associated with the clinical conditions such as convulsion activity, difficulties for oral hygiene behavior, walking problems and oral/digitalmanual habits. Bruxism is the most frequently observed oral habit in patients with Rett syndrome. Two cases with the Rett syndrome were reported. Both patients had the typical manifestations like stereotypic hand movement, bruxism and digit-hand sucking. Caries control for the patients was perfomed under general anesthesia.
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KEYWORD
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Rett syndrome, Stereotypic hand movement, Bruxism, General anesthesia
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